Intramedullary epidermoid cysts of the spinal cord

Case report

Alain Roux M.D. 1 , Claude Mercier M.D., F.R.C.S.(C) 1 , Albert Larbrisseau F.R.C.M.(C) 1 , Louis-Jacques Dube F.R.C.M.(C) 1 , Céline Dupuis F.R.C.M.(C) 1 and Raquel Del Carpio F.R.C.M.(C) 1
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  • 1 Departments of Neurosurgery, Neurology, Radiology, and Pathology, Sainte-Justine Hospital, University of Montreal, and Department of Radiology, Montreal Neurological Institute, Montreal, Quebec, Canada
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✓ Epidermoid cysts are tumors familiar to neurosurgeons, but intramedullary epidermoid cysts are rare. The authors report the case of a 6-year-old girl presenting with progressive paraparesis. A midthoracic intramedullary mass was revealed on myelography and magnetic resonance (MR) imaging and confirmed as an intramedullary epidermoid cyst at surgery, at which time the cyst was removed. This is the fourth report documenting a purely intramedullary epidermoid cyst occurring in a child. The pathology and etiology, epidemiology, clinical features, radiology (including MR image characteristics), and surgical treatment of such rare intramedullary benign tumors are discussed. Magnetic resonance imaging reduces the delay in diagnosis of spinal cord tumors but should be guided by clinical judgment.

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Contributor Notes

Address reprint requests to: Claude Mercier, M.D., Division of Neurosurgery, Sainte-Justine Hospital, 3175 Côte Ste-Catherine, Montreal, Quebec H3T 1C5, Canada.
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