Vertebral and epidural hemangioma with paraplegia in Klippel-Trenaunay-Weber syndrome

Case report

M. Gourie-Devi M.D., D.M.(Neuro.) 1 and Brahm Prakash M.S.(Surg.), M.Ch.(Neurosurg.) 1
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  • 1 Department of Neurology, Safdarjang Hospital and Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India
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✓ A patient with a rare case of Klippel-Trenaunay-Weber syndrome presented with paraplegia due to compression by a vertebral and epidural cavernous hemangioma. The metameric distribution of the large cutaneous vascular nevus provided the clinical clue to the nature of the spinal lesion. The association of the two lesions is explained on the basis of developmental anomaly.

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Contributor Notes

Address reprint requests to: M. Gourie-Devi, M.D., National Institute of Mental Health and Neuro Sciences, Post Bag 2779, Bangalore 560 029, India.
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