Omovertebral bone causing traumatic compression of the cervical spinal cord and acute neurological deficits in a patient with Sprengel’s deformity and Klippel-Feil syndrome: case report

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  • 1 Department of Orthopedic Surgery, St. Joseph’s University Medical Center, Paterson; and
  • 2 University Spine Center, Wayne, New Jersey
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The presence of an omovertebral bone with Sprengel’s deformity and Klippel-Feil syndrome is a complex congenital anomaly that is not well understood. It most commonly manifests as cosmetic deformity, limited range of motion, and functional disability, although there are reports of the insidious development of cervical myelopathy. In this paper, the authors present the case of a 49-year-old man with acute neurological deficits after a low-energy mechanism of traumatic spinal cord compression, resulting from an impinging omovertebral bone through a traumatic laminar defect. The patient underwent resection of the omovertebral bone, laminectomy decompression of the spinal canal, and anterior stabilization. This case highlights a rarely discussed complication of undiagnosed Sprengel’s deformity and its associated conditions following even low-energy traumatic mechanisms.

ABBREVIATIONS ACDF = anterior cervical decompression and fusion; AIS = American Spinal Injury Association Impairment Scale; ROM = range of motion.

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Contributor Notes

Correspondence Stuart Changoor: University Spine Center, Wayne, NJ. stuartchangoor@gmail.com.

INCLUDE WHEN CITING Published online September 25, 2020; DOI: 10.3171/2020.6.SPINE20304.

Disclosures The authors report no conflict of interest concerning the materials or methods used in this study or the findings specified in this paper.

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