Cervical rudimentary meningocele in adulthood

Case report

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Almost all cases of cervical spinal dysraphism published to date have involved cystic lesions and were treated in very early childhood. The authors describe a unique case of a 21-year-old woman who harbored a solid cervical rudimentary meningocele. On preoperative CT and MR images, a cutaneous solid mass was shown to be connected to intraspinal contents by a stalk traversing the C-3 lamina defect. The authors resected the cutaneous mass and released the tethering neural band from the vertical axis of the spinal cord without causing injury. Pathological examination demonstrated a dense collagenous tissue containing clusters of meningocytes and psammoma bodies in the cutaneous mass. This rare entity, a spinal dysraphism with a benign natural history, may contribute to the current classification of cervical spinal dysraphism.

Abbreviation used in this paper:CDCT = cystic spinal dysraphism of the cervical and upper thoracic region.

Article Information

Address correspondence to: Wenhua Yu, M.D., Department of Neurosurgery, Hangzhou First People's Hospital, Nanjing Medical University, Huan Sha Lu 261#, Hangzhou 310006, People's Republic of China. email: capsomerew@gmail.com.

Please include this information when citing this paper: published online March 15, 2013; DOI: 10.3171/2013.2.SPINE12603.

© AANS, except where prohibited by US copyright law.

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Figures

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    Appearance of the large posterior cutaneous mass (A), which caused the cosmetic problem. Note the purplish, poor-quality skin on its top and typical “hair collar” on the bottom. Cervical 3D CT scan (B) demonstrates a bony defect at the level of the C-3 lamina. Sagittal T1-weighted (C) and T2-weighted (D) MR images show a cutaneous solid mass connected to the intraspinal contents by a stalk traversing the lamina defect, in addition to a small CSF-filled cyst located beneath the tented neural band.

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    Intraoperative photograph (left) showing the stalk passed through the lamina defect with its dura-like integument, which was continuous with the normal intraspinal dura mater. Photomicrograph (right) demonstrating dense collagenous tissue containing clusters of meningocytes and a psammoma body (black arrow) in the cutaneous mass. H & E, original magnification ×200.

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