Cystic angiomatosis skull lesion obliteration with neuroendovascular sclerotherapy as a unique treatment: case report

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  • 1 Departments of Neurosurgery and
  • 2 Pathology and Laboratory Medicine, Medical University of South Carolina, Charleston; and
  • 3 Department of Neuroradiology and Neuroendovascular Surgery, Greenville Memorial Hospital, Greenville, South Carolina
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Cystic angiomatosis is a rare bone condition with complex presentation and difficult treatment. Current management strategies have poorly tolerated side effects and a low likelihood of disease eradication. The control of calvarial lesions that are symptomatic usually involves surgical excision and subsequent cranioplasty. This paradigm can present with a risk of morbidity and mortality depending on the anatomy of the lesion. Here, the authors present a novel approach to a difficult-to-treat occipital calvarial lesion directly overlying the transverse sinus, performing a small, partial-thickness craniectomy and alcohol sclerotherapy in a combined neurosurgery-neuroendovascular approach. At 3 years after treatment, the authors noted a complete, encouraging radiographic and clinical outcome.

ABBREVIATIONS CA = cystic angiomatosis; GSD = Gorham-Stout disease.

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Contributor Notes

Correspondence Guilherme B. F. Porto: Medical University of South Carolina, Charleston, SC. porto@musc.edu.

INCLUDE WHEN CITING Published online May 8, 2020; DOI: 10.3171/2020.3.PEDS2045.

Disclosures The authors report no conflict of interest concerning the materials or methods used in this study or the findings specified in this paper.

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