Endoscopic treatment of combined metopic-sagittal craniosynostosis

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  • 1 Division of Plastic & Reconstructive Surgery, Department of Surgery, and
  • 2 Department of Neurosurgery, Washington University School of Medicine in St. Louis; and
  • 3 Orthotic and Prosthetic Lab, St. Louis, Missouri
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OBJECTIVE

Combined metopic-sagittal craniosynostosis is traditionally treated with open cranial vault remodeling and fronto-orbital advancement, sometimes in multiple operations. Endoscopic treatment of this multisuture synostosis presents a complex challenge for the surgeon and orthotist.

METHODS

The authors retrospectively analyzed the preoperative and 1-year postoperative CT scans of 3 patients with combined metopic-sagittal synostosis, all of whom were treated with simultaneous endoscope-assisted craniectomy of the metopic and sagittal sutures followed by helmet therapy. Established anthropometric measurements were applied to assess pre- and postoperative morphology, including cranial index and interfrontal divergence angle (IFDA). Patients’ measurements were compared to those obtained in 18 normal controls.

RESULTS

Two boys and one girl underwent endoscope-assisted craniectomy at a mean age of 81 days. The mean preoperative cranial index was 0.70 (vs control mean of 0.82, p = 0.009), corrected postoperatively to a mean of 0.82 (vs control mean of 0.80, p = 0.606). The mean preoperative IFDA was 110.4° (vs control mean of 152.6°, p = 0.017), corrected postoperatively to a mean of 139.1° (vs control mean of 140.3°, p = 0.348). The mean blood loss was 100 mL and the mean length of stay was 1.7 days. No patient underwent reoperation. The mean clinical follow-up was 3.4 years.

CONCLUSIONS

Endoscope-assisted craniectomy with helmet therapy is a viable single-stage treatment option for combined metopic-sagittal synostosis, providing correction of the stigmata of trigonoscaphocephaly, with normalization of the cranial index and IFDA.

ABBREVIATIONS IFDA = interfrontal divergence angle; ZF-G-ZF angle = glabella and bilateral zygomaticofrontal sutures; ZF-ZF = interzygomaticofrontal.

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Contributor Notes

Correspondence Kamlesh B. Patel: Washington University in St. Louis, St. Louis, MO. kamlesh.patel@wustl.edu.

INCLUDE WHEN CITING Published online April 17, 2020; DOI: 10.3171/2020.2.PEDS2029.

Disclosures Dr. Patel is a consultant for Stryker CMF and an educational speaker for Hanger Clinic. Dr. Naidoo is an educational speaker for Hanger Clinic. Mr. Bellanger is an orthotist for Orthotic & Prosthetic Lab, Inc.

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