Currarino syndrome presenting as a cerebrospinal fluid leak from the dermal sinus tract: case report

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  • 1 Divisions of Pediatric Neurosurgery and
  • 2 Pediatric Surgery, Primary Children’s Hospital, University of Utah, Salt Lake City, Utah
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Currarino syndrome is an autosomal dominant condition with variable expressivity and penetrance that is associated with several classic features: sacral dysgenesis, presacral mass, and/or anorectal anomalies. The authors present a unique case in which the patient’s initial presentation was a CSF leak from a sinus tract. The sinus tract was identified and disconnected from the thecal sac, obliterating the anterior sacral meningocele. This case represents a unique scenario in which Currarino syndrome manifested as a CSF leak from a dermal sinus tract.

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Contributor Notes

Correspondence Douglas L. Brockmeyer: Primary Children’s Hospital, University of Utah, Salt Lake City, UT. neuropub@hsc.utah.edu.

INCLUDE WHEN CITING Published online March 6, 2020; DOI: 10.3171/2020.1.PEDS19692.

Disclosures The authors report no conflict of interest concerning the materials or methods used in this study or the findings specified in this paper.

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