Multidisciplinary staged surgical management of bifrontal meningoencephalocele with long-term follow-up

Case report

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  • Divisions of Neurosurgery (Pediatric Neurosurgery) and Plastic Surgery (UAB Cleft and Craniofacial Center), Children's of Alabama, University of Alabama at Birmingham, Alabama
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The authors report on an infant with a bifrontal encephalocele that was associated with multisuture craniosynostosis, spasticity, and a progressively severe epilepsy. They describe the initial presentation, genetic screening results, staged multidisciplinary operative plans, clinical course, complications, and long-term surgical and developmental follow-up. To their knowledge, the comprehensive surgical management of this type of complicated congenital cranial anomaly has not been previously described.

Surgical management was staged and multidisciplinary and required careful attention to all 3 components of the condition: 1) hydrocephalus, 2) frontal meningoencephalocele, and 3) epilepsy.

Abbreviations used in this paper:ACTH = adrenocorticotropic hormone; CGH = comparative genomic hybridization; EVD = external ventricular drain; VP = ventriculoperitoneal.

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Contributor Notes

Address correspondence to: Jeffrey P. Blount, M.D., Division of Pediatric Neurosurgery, JLB 400, 1600 7th Avenue South, Birmingham, Alabama 35233. email: jeffrey.blount@childrensal.org.

Please include this information when citing this paper: published online January 25, 2013; DOI: 10.3171/2012.11.PEDS12330.

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