Coexistence of dermal sinus tract, dermoid cyst, and encephalocele in a patient presenting with nasal cellulitis

Case report

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  • 1 Departments of Neurosurgery and
  • 2 Otolaryngology, Children's Hospital of Pittsburgh of the University of Pittsburgh Medical Center; and
  • 3 Department of Pathology, University of Pittsburgh Medical Center—Presbyterian Hospital, Pittsburgh, Pennsylvania
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Dermoid cysts, encephaloceles, and dermal sinus tracts represent abnormalities that develop during the process of embryogenesis. The elucidation of the precise timing of formation for these malformations has remained elusive at the molecular level of study. Yet, clinical experience has demonstrated that these malformations do not all occur in the same patient, suggesting a shared pathway that goes awry at distinct points for different patients, resulting in 1 of the 3 malformations. Herein the authors describe a case in which all 3 malformations were present in a single patient. This is the first description in the English literature of a sincipital encephalocele occurring with a dermoid cyst and a dermal sinus tract.

Abbreviation used in this paper:GFAP = glial fibrillary acidic protein.

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Contributor Notes

Address correspondence to: Mahesh Karandikar, M.D., Ph.D., Children's Hospital of Pittsburgh, Department of Pediatric Neurosurgery, Children's Hospital Drive, 45th Street and Penn Avenue, Pittsburgh, Pennsylvania 15201. email: mahesh7069@gmail.com.

Please include this information when citing this paper: published online November 9, 2012; DOI: 10.3171/2012.10.PEDS12335.

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