Intraventricular chordoid meningioma in a child: fever of unknown origin, clinical course, and response to treatment

Case report

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The authors present the case of an 11-year-old boy with an intraventricular chordoid meningioma, which is a rare presentation of prolonged fever of unknown origin due to a rare tumor in a rare location. The fever resolved after excision of the lesion. Subsequent imaging revealed recurrence at 1 year. After a repeat excision and fractionated radiotherapy, the patient has remained disease free 5 years after the first surgery. Very few cases of intraventricular chordoid meningioma have been reported to date. The pathological features and clinical course are described. A review of the literature describing management options for this tumor type, recently found to have a higher recurrence rate, is described herein.

Abbreviations used in this paper:EMA = epithelial membrane antigen; FUO = fever of unknown origin.
Article Information

Contributor Notes

Address correspondence to: Ashok Pillai, M.D., D.N.B. (Neurosurgery), Department of Neurosurgery, Amrita College of Medicine, Elamakkara P.O., Edapally, Ernakulam, Kerala, India 682 026. email: brashok@aims.amrita.edu.Please include this information when citing this paper: published online October 12, 2012; DOI: 10.3171/2012.9.PEDS11398.

© AANS, except where prohibited by US copyright law.

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