Thoracolumbar spinal deformity in achondroplasia

Full access

The authors review the management of thoracolumbar kyphotic deformity in cases of achondroplasia. The presence of angular thoracolumbar kyphosis in achondroplasia is well recognized. In children this is initially a nonfixed deformity that persists, however, in more than 10% of individuals and becomes a fixed thoracolumbar kyphotic deformity. Additionally, with the coexistent spinal canal stenosis, neurological damage can occur and manifest as spinal cord or cauda equina compression. The nature of this condition, the natural history, and management options are discussed. Anatomical and biomechanical factors relevant to the condition are specifically highlighted. Avoidance of pitfalls in the management of these patients is discussed for both pediatric and adult patients.

Abbreviations used in this paper:AP = anteroposterior; CT = computerized tomography; FGF = fibroblast growth factor; MR = magnetic resonance; TLSO = thoracolumbosacral orthosis.

The authors review the management of thoracolumbar kyphotic deformity in cases of achondroplasia. The presence of angular thoracolumbar kyphosis in achondroplasia is well recognized. In children this is initially a nonfixed deformity that persists, however, in more than 10% of individuals and becomes a fixed thoracolumbar kyphotic deformity. Additionally, with the coexistent spinal canal stenosis, neurological damage can occur and manifest as spinal cord or cauda equina compression. The nature of this condition, the natural history, and management options are discussed. Anatomical and biomechanical factors relevant to the condition are specifically highlighted. Avoidance of pitfalls in the management of these patients is discussed for both pediatric and adult patients.

If the inline PDF is not rendering correctly, you can download the PDF file here.

Article Information

Address reprint requests to: Sanjay N. Misra, M.D., K3-159, 4480 Oak Street, Vancouver V64 3X2, British Columbia, Canada.

© AANS, except where prohibited by US copyright law.

TrendMD

Metrics

Metrics

All Time Past Year Past 30 Days
Abstract Views 0 0 0
Full Text Views 157 156 8
PDF Downloads 224 208 10
EPUB Downloads 0 0 0

PubMed

Google Scholar