Successful stent placement for cervical artery dissection associated with the Ehlers—Danlos syndrome

Case report and review of the literature

Akira Kurata Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Hidehiro Oka Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Taketomo Ohmomo Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Hitoshi Ozawa Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Sachio Suzuki Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Kiyotaka Fujii Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Shinichi Kan Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Yoshio Miyasaka Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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Harue Arai Departments of Neurosurgery, Radiology, and Dermatology, Kitasato University School of Medicine, and Yamato Municipal Hospital, Kanagawa, Japan

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1077–1081
Volume/Issue:
Volume 99: Issue 6
DOI link:
https://doi.org/10.3171/jns.2003.99.6.1077
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✓ This 44-year-old man with Ehlers—Danlos syndrome (EDS) Type IV presented with hemiparesis and the Gerstmann syndrome. Left carotid artery (CA) angiography revealed a dissecting aneurysm with severe stenosis located in the common CA; the lesion was successfully treated with a stent graft. The patient's clinical course after endovascular surgery was uneventful, without occurrence of megacolon. The literature for spontaneous CA dissection in EDS Type IV cases is reviewed and points for investigation and treatment are discussed.

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Contributor Notes

Address reprint requests to: Akita Kurata, M.D., Department of Neurosurgery, Kitasato University School of Medicine, 1–15–1 Kitasato, Sagamihara, Kanagawa, Japan. email: akirak@med.kitasato-u.ac.jp.
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