✓ The management of congenital scalp and skull defects, as generally advocated, is surgical. The authors report such a case that was treated conservatively. At her 3-year follow-up review, the patient's scalp and skull defects and other associated cutaneous defects were fully reconstituted. Such a nonoperative approach, while rarely reported, emphasizes the natural course that some of these lesions may follow. The literature on aplasia cutis congenita is briefly reviewed.
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Anderson CE, , Hollister D, & Szalay GC: Autosomal dominantly inherited cutis aplasia congenita, ear malformations, right-sided facial paresis, and dermal sinuses. Birth Defects 15 ( 5B): 265–270, 1979 Anderson CE, Hollister D, Szalay GC: Autosomal dominantly inherited cutis aplasia congenita, ear malformations, right-sided facial paresis, and dermal sinuses. Birth Defects 15 (5B):265–270, 1979
Bart BJ, , Gorlin RJ, & Anderson VE, et al: Congenital localized absence of skin and associated abnormalities resembling epidermolysis bullosa. A new syndrome. Arch Dermatol 93:296–304, 1966 Bart BJ, Gorlin RJ, Anderson VE, et al: Congenital localized absence of skin and associated abnormalities resembling epidermolysis bullosa. A new syndrome. Arch Dermatol 93:296–304, 1966
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Campbell W: Case of congenital ulcer on the cranium of a fetus, terminating in fatal hemorrhage on the 18th day after birth. Edinb J Med Sci 2:82–83, 1826 Campbell W: Case of congenital ulcer on the cranium of a fetus, terminating in fatal hemorrhage on the 18th day after birth. Edinb J Med Sci 2:82–83, 1826
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Croce EJ, , Purohit RC, & Janovski NA: Congenital absence of skin (aplasia cutis congenita). Arch Surg 106:732–734, 1973 Croce EJ, Purohit RC, Janovski NA: Congenital absence of skin (aplasia cutis congenita). Arch Surg 106:732–734, 1973
Cutlip BD Jr, , Cryan DM, & Vineyard WR: Congenital scalp defects in mother and child. Am J Dis Child 113:597–599, 1967 Cutlip BD Jr, Cryan DM, Vineyard WR: Congenital scalp defects in mother and child. Am J Dis Child 113:597–599, 1967
Deeken JH, & Caplan RM: Aplasia cutis congenita. Arch Dermatol 102:386–389, 1970 Deeken JH, Caplan RM: Aplasia cutis congenita. Arch Dermatol 102:386–389, 1970
Demmel U: Clinical aspects of congenital skin defects. I. Congenital skin defects on the head of the newborn. Eur J Pediatr 121:21–50, 1975 Demmel U: Clinical aspects of congenital skin defects. I. Congenital skin defects on the head of the newborn. Eur J Pediatr 121:21–50, 1975
Farmer AW, & Maxmen MD: Congenital absence of skin. Plast Reconstr Surg 25:291–297, 1960 Farmer AW, Maxmen MD: Congenital absence of skin. Plast Reconstr Surg 25:291–297, 1960
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Fowler GW, & Dumars KW: Cutis aplasia and cerebral malformation. Case report. Pediatrics 52:861–864, 1973 Fowler GW, Dumars KW: Cutis aplasia and cerebral malformation. Case report. Pediatrics 52:861–864, 1973
Fryns JP, & Van den Berghe H: Congenital scalp defects associated with postaxial polydactyly. Hum Genet 49:217–219, 1979 Fryns JP, Van den Berghe H: Congenital scalp defects associated with postaxial polydactyly. Hum Genet 49:217–219, 1979
Ingalls NW: Congenital defects of the scalp. Studies in the pathology of development, III. Am J Obstet Gynecol 25:861–873, 1933 Ingalls NW: Congenital defects of the scalp. Studies in the pathology of development, III. Am J Obstet Gynecol 25:861–873, 1933
Johnsonbaugh RE, , Light IJ, & Sutherland JM: Congenital scalp defects in father and son. Am J Dis Child 110:297–298, 1965 Johnsonbaugh RE, Light IJ, Sutherland JM: Congenital scalp defects in father and son. Am J Dis Child 110:297–298, 1965
Kahn EA, & Lemmen LJ: Unusual congenital anomalies of neurosurgical interest in infants and children. J Neurosurg 7:544–554, 1950 Kahn EA, Lemmen LJ: Unusual congenital anomalies of neurosurgical interest in infants and children. J Neurosurg 7:544–554, 1950
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Kaiser IH: Aplasia cutis congenita. Am J Obstet Gynecol 130:503, 1978 (Letter) Kaiser IH: Aplasia cutis congenita. Am J Obstet Gynecol 130:503, 1978 (Letter)
Keipert JA: Congenital scalp defects in brother and sister. Med J Aust 1:866–868, 1972 Keipert JA: Congenital scalp defects in brother and sister. Med J Aust 1:866–868, 1972
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Matson DD: Neurosurgery of Infancy and Childhood. Springfield, Ill: Charles C Thomas, 1969, pp 168–173 Matson DD: Neurosurgery of Infancy and Childhood. Springfield, Ill: Charles C Thomas, 1969, pp 168–173
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Rudolph RI, , Schwartz W, & Leyden JJ: Bitemporal aplasia cutis congenita. Occurrence with other cutaneous abnormalities. Arch Dermatol 110:615–618, 1974 Rudolph RI, Schwartz W, Leyden JJ: Bitemporal aplasia cutis congenita. Occurrence with other cutaneous abnormalities. Arch Dermatol 110:615–618, 1974
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Vinocur CD, , Weintraub WH, & Wilensky RJ, et al: Surgical management of aplasia cutis congenita. Arch Surg 111:1160–1164, 1976 Vinocur CD, Weintraub WH, Wilensky RJ, et al: Surgical management of aplasia cutis congenita. Arch Surg 111:1160–1164, 1976
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