Mesencephalic spur (beaking deformity of the tectum) in Arnold-Chiari malformation

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✓ The beaking deformity of the tectum, referred to in this paper as the mesencephalic spur, is regularly present in the Type II variety of the Arnold-Chiari malformation in varying degrees of severity. When the mesencephalic spur is related to associated myelomeningocele, it was found that the more extensive the myelomeningocele, and the older the affected children, the more prominent was the mesencephalic spur.

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Address reprint requests to: Adelola Adeloye, M.R.C.P., F.R.C.S., Neurosurgical Unit, Department of Surgery, University of Ibadan, Ibadan, Nigeria.

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Figures

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    Dorsal view of normal brain stem showing the four normal colliculi, with part of the pineal gland (p) above the superior pair.

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    Lateral view showing a mild degree of mesencephalic spur (s) with gross preservation of the four colliculi, in a baby boy who died at 3 days.

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    Spur (s) with preservation of the superior colliculi (u) only.

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    Mesencephalic spur (arrow) and its relation to the cerebellum (c).

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    Left: Severe beaking deformity in a 4-week-old boy with hydrocephalus. Note the sharp midline ridge (r). Right: Prominent mesencephalic spur in a 1½-year-old hydrocephalic girl. Note stretching of the pineal gland (p) above the spur.

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