Thoracic cord compression due to chondrosarcoma in two cousins with hereditary multiple exostoses

Report of two cases

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✓ Two teen-age male cousins with hereditary multiple exostoses developed cord compression secondary to chondrosarcoma. The clinical presentation, diagnostic work-up, surgical treatment, pathological findings, and postoperative course are described in each patient.

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Address reprint requests to: James Wepsic, M.D., Neurosurgical Service, Massachusetts General Hospital, Boston, Massachusetts 02114.

© AANS, except where prohibited by US copyright law.

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Figures

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    Case 1. Exostoses of the right femur (left), humerus (center), and ulna and radius (right).

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    Case 1. Thoracic Pantopaque myelogram demonstrating complete block at T-2.

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    Case 1. Photomicrograph of the tumor showing hypercellular tissue with variability in the size and shape of the lacunae and chondrocytes. Normal cartilaginous architecture is lacking. Osteoid formation (upper left), calcification, and hemorrhage (lower left) are present. Pathological diagnosis was low-grade chondrosarcoma. H & E, × 100.

References

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