✓The authors report on the case of a craniopharyngioma arising in the cerebellopontine angle (CPA) in a patient with Gardner syndrome. Although familial adenomatous polyposis (FAP) is associated with intracranial neoplasms, the current case is only the third reported craniopharyngioma in a patient with Gardner syndrome. Two of these tumors, including that of the current case, originated in the CPA, an unusual location for craniopharyngiomas. The literature concerning FAP and its associations with intracranial neoplasia, as well as the pathogenesis of craniopharyngiomas in the posterior fossa, is discussed.
Abbreviations used in this paper:CNS = central nervous system; CPA = cerebellopontine angle; FAP = familial adenomatous polyposis; MR = magnetic resonance.
CiricISRegional embryology and developmental anatomy of the third ventricle, pituitary gland and the lesions of the area. ApuzzoMLJ: Surgery of the Third Ventricle ed 2BaltimoreWilliams & Wilkins1998. 159–166
CiricIS, Regional embryology and developmental anatomy of the third ventricle, pituitary gland and the lesions of the area. ApuzzoMLJ: Baltimore, Williams & Wilkins, 1998. 159–166)| false
JanzerRCBurgerPCGiangasperoFPaulusWCraniopharyngioma. KleihuesPCaveneeWK: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Nervous SystemLyonIARC Press2000. 244–246